| CASE REPORT |
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| Year : 2014 | Volume
: 9
| Issue : 2 | Page : 124-126 |
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Successful management of bilateral refractory chylothorax after double lung transplantation for lymphangioleiomyomatosis
Mohammed Hussein1, Yasser M Aljehani2, Imran Nizami2, Waleed Saleh2
1 Department of Surgery, King Faisal Specialist Hospital & Research Center, Riyadh, Saudi Arabia; Department of Cardiothoracic Surgery, Ain Shams University, Cairo, Egypt
2 Department of Surgery, King Faisal Specialist Hospital & Research Center, Riyadh, Saudi Arabia
Correspondence Address:
Yasser M Aljehani
Department of Surgery, King Faisal Specialist Hospital & Research Center, Riyadh, Saudi Arabia
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DOI: 10.4103/1817-1737.128862 PMID: 24791177 
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Lymphangioleiomyomatosis (LAM) is a rare disease that leads to airways and lymphatic channels obstruction due to abnormal smooth muscle proliferation. It presents with dyspnea, pneumothorax or chylothorax. Lung transplantation (LT) has emerged as a valuable therapeutic option with limited reports. We report a case of LAM that underwent double LT and complicated by refractory bilateral chylothorax which was managed successfully by povidone-iodine pleurodesis and the addition of sirolimus to the post-transplantation immunosuppressive therapy. The patient has no recurrence with 24 months follow-up. |
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